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(pathology) Cystic fibrosis.

Cystic fibrosis – Mucoviscidosis – Medical genetics, pulmonology – Difficulty breathing, coughing up mucus, poor growth, fatty stool – Symptoms recognizable ~6 months – Long term – Genetic (autosomal recessive) – Genetic – Sweat test, genetic testing – Physiotherapy, antibiotics, pancreatic enzyme replacement, cystic fibrosis transmembrane conductance regulator modulators, lung transplantation – Life expectancy between 42 and 50 years (developed world) – 1 out of 3,000 (Northern European).

(pathology) Cystic fibrosis.

Health problems associated with cystic fibrosis

(pathology) Cystic fibrosis.

Respiratory infections in CF vary according to age. Green = Pseudomonas aeruginosa Brown = Staphylococcus aureus Blue = Haemophilus influenzae Red = Burkholderia cepacia complex